Ohvira Syndrome: Case Report

Abstract

OHVIRA syndrome (Obstructed Hemivagina and Ipsilateral Renal Anomaly), secondary to Müllerian malformation, is a rare pathology, previously known as Herlyn-Werner-Wunderlich syndrome, characterized by the classic triad of didelphys uterus, obstructed hemivagina and ipsilateral renal agenesis. Clinically, it manifests itself more frequently in adolescence, with pelvic pain, sensation of vaginal mass, dysmenorrhea, and irregularity in menstrual cycles. The diagnosis is confirmed ultrasonographical or by magnetic resonance imaging and its treatment is mainly surgical. With delayed diagnosis, different complications occur such as infertility and abortions. A clinical case of a 10-year-old patient with multiple pathologies is presented, with clinical symptoms of right renal agenesis, uterus didelphys and repetitive symptoms of hematocolpos due to hemivaginal obstruction.